Wegener's Granulomatosis Vasculitis and Granuloma: A Case Report Wegener's Granulomatosis
Journal of Pediatric Nephrology,
Vol. 9 No. 3 (2021),
4 September 2021
,
Page 1-3
https://doi.org/10.22037/jpn.v9i3.34117
Abstract
A 13-year-old girl was admitted to our hospital because of fatigue, oliguria, and edema of lower extremities. Her laboratory workup showed an acute renal failure (BUN= 225 mg/dl, Creatinine= 13.25 mg/dl). She also had a massive proteinuria.
A renal biopsy showed cellular crescentic glomerulonephritis and positive C-ANCA. The serum Creatinine level decreased after treatment with high-dose methylprednisolone, rituximab and plasmapheresis. She did not require dialysis.
This is a report of a rare case of GPA presenting with 100% cellular crescentic glomerulonephritis.
- Pauci-Immune Necrotizing Glomerulonephritis
- Crescentic Glomerulonephritis
- Wegener's Granulomatosis
- Child
How to Cite
References
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