The Effect of Concurrent Use of Lower Extremity and Spinal Orthotics Intervention to Improve Activity Daily Living and Quality Of Life in Charcot-Marie-Tooth Disease: A Single-Subject Design
Journal of Clinical Physiotherapy Research,
Vol. 4 No. 2 (2019),
7 July 2020
,
Page e10
https://doi.org/10.22037/jcpr.v4i4.29310
Abstract
Introduction: The Charcot-Marie-Tooth (CMT) disease causes the significant muscular deficits in the affected patients, inhibits activities daily living, and involves a severe disability. The aim of this study was to evaluate the effect of concurrent use of a knee-ankle foot orthosis along with a body jacket orthosis to improve activities daily living in a person with CMT. Methods and Materials: A boy aged 16 years old with CMT was evaluated in this case report. He had a sever Kypho-scoliosis deformity in his spine and sever equines in his feet with unstable knee. In order to control of knees and ankles simultaneously, an ankle foot orthosis with the supracondylar trimline was designed. The control of his sever spinal deformity was also provided by a body jacket over shoulder. To evaluation of activities daily living, subject was asked to filled Barthel index out during a week. After one month, the individual was asked to fill the Barthel index out again. Finally, user friendly of orthotics were evaluated by a satisfaction questionnaire. Results: The results indicated that the orthoses was capable to improve activity daily living (25 percent increase after using orthosis in Barthel index). Also, results showed 30 percent increase after using orthosis for the QOL questionnaire. The mean of scale in satisfaction questionnaire were 4.5 based on Likert scale. Conclusion: This single-case study demonstrated the control of spinal and lower limb is simultaneously necessary for the improvement of activity daily living.
Key words: ADL, QOF, Charcot-Marie-Tooth, Orthotics And Spinal Deformity
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References
References:
Brooke M. The symptoms and signs of neuromuscular diseases. A clinicians view of neuromuscular diseases, Williams and Wilkins, Baltimore. 1977:1-33.
Dyck P. Hereditary motor and sensory neuropathies. Peripheral neuropathy. 1993:1094-136.
Charcot JM. Sur une forme paticuliere d'atrophie musuculaire progressive souvent familial, debutante par les pieds et les jambes et atteignant plus tard les mains. Rev Med Fr. 1886;6:97-138.
R. M. Infant neuropsychiatry. . edition. t, editor. Naples, Italy: Edizioni Idelson-Gnocchi; 2009.
Vinci P, Serrao M, Millul A, Deidda A, De Santis F, Capici S, et al. Quality of life in patients with Charcot–Marie–Tooth disease. Neurology. 2005;65(6):922-4.
Taniguchi JB, Elui V, Osorio FL, Hallak JE, Crippa JA, Machado-de-Sousa JP, et al. Quality of life in patients with Charcot-Marie-Tooth disease type 1A. Arquivos de neuro-psiquiatria. 2013;71(6):392-6.
Kenis-Coskun O, Matthews DJ. Rehabilitation issues in Charcot-Marie-Tooth disease. Journal of pediatric rehabilitation medicine. 2016;9(1):31-4.
Njegovan ME, Leonard EI, Joseph FB. Rehabilitation medicine approach to Charcot-Marie-Tooth disease. Clinics in podiatric medicine and surgery. 1997;14(1):99-116.
Bean J, Walsh A, Frontera W. Brace modification improves aerobic performance in Charcot-Marie-Tooth disease: a single-subject design. American journal of physical medicine & rehabilitation. 2001;80(8):578-82.
Menotti F, Laudani L, Damiani A, Mignogna T, Macaluso A. An anterior ankle-foot orthosis improves walking economy in Charcot–Marie–Tooth type 1A patients. Prosthetics and orthotics international. 2014;38(5):387-92.
Morris C. A review of the efficacy of lower-limb orthoses used for cerebral palsy. Developmental medicine and child neurology. 2002;44(3):205-11.
Shah S, Vanclay F, Cooper B. Improving the sensitivity of the Barthel Index for stroke rehabilitation. Journal of clinical epidemiology. 1989;42(8):703-9.
de Morton NA, Keating JL, Davidson M. Rasch analysis of the Barthel Index in the assessment of hospitalized older patients after admission for an acute medical condition. Archives of physical medicine and rehabilitation. 2008;89(4):641-7.
Almenara M, Cempini M, Gómez C, Cortese M, Martín C, Medina J, et al. Usability test of a hand exoskeleton for activities of daily living: an example of user-centered design. Disability and Rehabilitation: Assistive Technology. 2017;12(1):84-96.
Wuensch KL. What is a Likert Scale. And How Do You Pronounce'Likert. 2005.
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