Anesthetic Considerations in a Patient With Plexiform Neurofibromatosis: A Case Report
International Clinical Neuroscience Journal,
Vol. 5 No. 4 (2018),
20 December 2018
,
Page 169-170
Abstract
Plexiform neurofibromatosis is an uncommon variant of neurofibromatosis type 1 (NF1) (Von Recklinghausen’s disease). There is a greater prevalence of neurofibromatosis 1 in patients with other neoplasms, such as rhabdomyosarcomas, gastrointestinal stromal tumors (GISTs), pheochromocytomas, carcinoid tumors and ganglioneuromas. We report the anesthetic implications of a case of a 33 year old patient with plexiform neurofibromatosis and a history of pheochromocytoma which was operated on previously. He presented with painless swelling on upper eye-lead since childhood and had multiple café-au-lait spots and neurofibromas on the trunk. The surgery was done in two sessions first on the plexiform neurofibroma of the eye followed by the operation on the brain mass.- Plexiform neurofibromatosis
- Anesthetic implications
- Pheochromocytoma.
How to Cite
References
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