International Clinical Neuroscience Journal

Vol. 5 No. 4 (2018)

Anesthetic Considerations in a Patient With Plexiform Neurofibromatosis: A Case Report

International Clinical Neuroscience Journal, Vol. 5 No. 4 (2018), 20 December 2018 , Page 169-170

Abstract

Plexiform neurofibromatosis is an uncommon variant of neurofibromatosis type 1 (NF1) (Von Recklinghausen’s disease). There is a greater prevalence of neurofibromatosis 1 in patients with other neoplasms, such as rhabdomyosarcomas, gastrointestinal stromal tumors (GISTs), pheochromocytomas, carcinoid tumors and ganglioneuromas. We report the anesthetic implications of a case of a 33 year old patient with plexiform neurofibromatosis and a history of pheochromocytoma which was operated on previously. He presented with painless swelling on upper eye-lead since childhood and had multiple café-au-lait spots and neurofibromas on the trunk. The surgery was done in two sessions first on the plexiform neurofibroma of the eye followed by the operation on the brain mass.
Keywords:
  • Plexiform neurofibromatosis
  • Anesthetic implications
  • Pheochromocytoma.

How to Cite

1.
Soltanpoor P, Behnaz F, Farokhi M, Jalili Khoshnood R, Azizi Farsani HR. Anesthetic Considerations in a Patient With Plexiform Neurofibromatosis: A Case Report. Int Clin Neurosci J [Internet]. 2018 Dec. 20 [cited 2025 Jul. 9];5(4):169-70. Available from: https://journals.sbmu.ac.ir/neuroscience/article/view/24128

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