Myotonic Dystrophy and Volvulus: Anesthetic Considerations For an Urgent Situation And the Role of Sugammadex; A Case Report Myotonic dystrophy and sugammadex
Journal of Cellular & Molecular Anesthesia,
Vol. 7 No. 3 (2022),
11 July 2022
,
Page 187-190
https://doi.org/10.22037/jcma.v7i2.32945
Abstract
Myotonic dystrophy (MD), although not a common disorder, is a challenge for anesthesiologists as it restricts choices of medication and involves some organs other than muscles. Here we report a known case of MD underwent laparatomy for bowel obstruction. Anesthesia was induced rapidly and muscle relaxation achieved by using high dose of rocuronium. Reversal of muscle relaxation was done with sugammadex successfully with no residual relaxation. Rocuronium could be used as a safe mean of rapid muscle relaxation in MD and reversal could be achieved with sugammadex.
- Myotonic dystrophy, steinert disease, sugammadex, rocuronium
How to Cite
References
Koyama Y, Kohno M, Tsuzaki K, Kamiyama K, Morimoto Y. Bilevel positive airway pressure therapy in a patient with myotonic dystrophy and postoperative respiratory failure: A case report. Saudi J Anaesth. 2020;14(2):241-3.
Gandhi R, Jain AK, Sood J. Desflurane anaesthesia in myotonic dystrophy. Indian J Anaesth. 2011;55(1):61-3.
Gorelik L, Flores A. Anesthetic Management for Multiple Family Members with Myotonic Dystrophy for Interventional Cardiac Procedures-A Case Series. Front Med (Lausanne). 2017;4:243.
Aldridge LM. Anaesthetic problems in myotonic dystrophy. A case report and review of the Aberdeen experience comprising 48 general anaesthetics in a further 16 patients. Br J Anaesth. 1985;57(11):1119-30.
Hannon VM, Cunningham AJ, Hutchinson M, McNicholas W. Aspiration pneumonia and coma--an unusual presentation of dystrophic myotonia. Can Anaesth Soc J. 1986;33(6):803-6.
Sinclair JL, Reed PW. Risk factors for perioperative adverse events in children with myotonic dystrophy. Paediatr Anaesth. 2009;19(8):740-7.
Najid NM, Razak TA, Gunaydin DB. Analgesia and Anaesthesia Management of Labour and Caesarean Delivery for a Parturient with Paramyotonia Congenita. Turk J Anaesthesiol Reanim. 2019;47(4):345-7.
Gaszynski T. Opioid-free general anesthesia in patient with Steinert syndrome (myotonic dystrophy): Case report. Medicine (Baltimore). 2016;95(37):e4885.
Grijalba Ipinazar I, Tuduri Limousin I, Reguera Fernandez M, Najarro Ajuria G, Martinez Ruiz A. Anesthetic management of a child with congenital Steiner syndrome scheduled for laparoscopic bilateral orchidopexy. Rev Esp Anestesiol Reanim. 2019;66(7):381-4.
Bombelli F, Lispi L, Porrini SC, Giacanelli M, Terracciano C, Massa R, et al. Neuromuscular transmission abnormalities in myotonic dystrophy type 1: A neurophysiological study. Clin Neurol Neurosurg. 2016;150:84-8.
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