A 21 Years Old Woman, with Chest Pain and Cardiac Dextroposition Pulmonary Hypoplasia or Scimitar Syndrome?
International Journal of Medical Toxicology and Forensic Medicine,
Vol. 2 No. 3(Summer) (2012),
12 January 2013
,
Page 110-112
https://doi.org/10.22037/ijmtfm.v2i3(Summer).3952
Abstract
Background: Physicians seldom encounter chest x-ray of adult patients diagnosed with dextrocardia.
Case presentation: Here, we present the case of a 21-year-old woman who referred to the hospital with the clinical diagnosis of dextrocardia but, she has pulmonary hypoplasia and this rare disease in adults may be a component of scimitar syndrome and scimitar sign is not pathognomonic to define the syndrome. MR angiography was done, but finally the diagnosis was hypoplasia of right upper lobe and aplasia of middle lobe.
Conclusion: As lung hypoplasia is rare in adults, some cases are misdiagnosed as dextrocardia on chest x-ray.
- Lobar Aplasia
- Hypoplasia
- Scimitar Syndrome
- Cardiac Dextroposition
- Agenesia
How to Cite
References
Qin JS, Gao Y, Pan MX. Single-port transumbilical laparoscopic cholecystec-tomy in an adult patient with congenital pulmonary hypoplasia: a case report. Nan Fang Yi Ke Da Xue Xue Bao. 2011;31(8):1334-5.
Akhavan-Heidari M, Edwards D, Besenhav.er J, Wolfer R. Incidental finding of congenital thoracic malformations in adult population. South Med J. 2006;99(5):539-43.
Mendeloff EN. Squestrations, congential cystic adenmatoid malformations, and congenital lobar emphysema. Semin thorac cardiovase surg. 2004;16(3):209-214.
Kisku Kh. Agenesis of lung-Acase report. Lung India .2008. 25(1):28-30.
Shanmugam G. Adult congenital lung disease. Eur J cardiothorac surg. 2005;28(3)483-9.
Berrocal T, Madrid C, Novo S, Gutierrez J, Arjonilla A, Gomezx-leon N. Congenital anomalies of the tracheobronchial tree, lung and mediastinum. Embryology, radiology, and pathology, radiographic. 2004;24(1):17-23.
Zylak CJ, Eyler WR, Spizamy DL, Stone CH. Department of diagnostic radiology henry ford hospital. Radiographics. 2002; 12(4):525-43.
Midyat L, Demir E, Askin M, Gulen F, Ulger Z, Tanc R, Bayraktaroglu S. Eponym: Scimitar syndrome. Eur J pediatr. 2010;4(3)21-18.
Gudjonsson U, Brown JW. Semin thorac cardiovasc surg pediatr card surg annu, 2006. 11(3):56-62.
Vida V, Speggirion S, Padaline MA, Crupi G, Marcelletti C, Zannini L, Frigiola A, Varrica A, Di-Cario D, Di Donato R, Murzi B, Berrabei M, Boccuzzo G, Stellin G. The scimitar syndrome: an Italian multicenter study. Ann thorac surg. 2009;88(2):440-4.
Arcieri L, Margaryan R, Murzi M, Cantinotti M, Murzi B.Repair of Partial Anomalous Pulmonary Venous Connection in the Scimitar Syndrome Using Vacuum-Assisted Venous Drainage. J Card Surg. 2012;10(2)43-47.
Alfano R.calcaterra G, Garaffa D, Basile G, spataro G. Speradeo v. Scimitar syn drome with or without the 'scimitar sign'] . Article in Italian. Pediatr Med chir. 1982;4(3):291-6.
- Abstract Viewed: 326 times
- PDF Downloaded: 383 times