Iranian Endodontic Journal

Abstract

Noonan syndrome is a genetic condition characterized by various systemic issues, including cardiac defects, short stature, bleeding problems, and intellectual disabilities. This disorder also shows several manifestations in the oral and maxillofacial region, highlighting the dentist’s role in diagnosing and addressing related complications. This report represents the effective dental management of a 15-year-old boy with Noonan syndrome who suffered from several oral and dental problems and was clinically and radiographically asymptomatic in a nine-month follow-up session. Awareness of the medical conditions and orofacial manifestations of patients with Noonan syndrome can be effective in determining a better treatment plan, providing more effective and safer treatment, and subsequently enhancing the long-term prognosis.