Familial Dysautonomia, Report of 3 Cases from Iran and a Discussion about Their General and Anaesthesia Care
Novelty in Biomedicine,
Vol. 3 No. 2 (2015),
12 April 2015
,
Page 94-98
https://doi.org/10.22037/nbm.v3i2.8680
Abstract
Background: Familial Dysautonomia (FD) is a rare hereditary syndrome which is an autosomal recessive trait that typically affects Jewish children. Important signs and symptoms of the disorder include; diminished pain perception, absence of overflow tears, hypotonia, fainting cardiac arrhythmias and autonomic crisis.Cases Report: In this article we reported 3 cases of FD syndrome which had presented for surgical operation followed by a discussion about general care of these patients as well as Anesthesia considerations.
- Familial Dysautonomia
- Pain
- Anesthesia care
How to Cite
References
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