Isolated Penopubic Continent Epispadias in Children. A Case Series.
Iranian Journal of Pediatric Surgery,
Vol. 12 No. 1 (2026),
20 Ordibehesht 2026
,
Page 102 - 110
https://doi.org/10.22037/irjps.v12i1.46585
Abstract
Isolated male epispadias (IME) is a rare entity with incidence of approximately 1 in 120,000 live births. Continent epispadias is an extremely rare entity with an incidence of less than 10percent of all cases. It is characterized by failure of the urethral plate to tabularize on the dorsum of the penis with defect ranging from glandular to penopubic region.The greatest challenge in treating epispadias is creating adequate penile length, straightening of penis and a penopubic angle that would allow comfortable penile penetration. A total of three male patient aged 6, 8 and 9 years with continent isolated penopubic epispadias underwent surgical repair with Modified Cantwell-Ransley reconstruction procedure. Postoperatively, there was no fistula and urine stream through neomeatus was adequate and the shape of the penis was cosmetically acceptable.
- Isolated Male Epispadias (IME), Modified Cantwell-Ransley repair, Bladder exostrophy epispadias complex (BEEC).
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References
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