Anesthesia management in a pediatric patient with Prune belly syndrome; a case report
Iranian Journal of Pediatric Surgery,
Vol. 8 No. 2 (2022),
26 October 2022
,
Page 173-178
https://doi.org/10.22037/irjps.v8i2.33869
Abstract
Prune belly syndrome (PBS) is a rare congenital disorder, consists of three symptoms: anterior abdominal muscle deficiency, cryptorchidism, and genitourinary malformation. These patients have cardiovascular and musculoskeletal abnormalities, mental retardation, chest deformities, and scoliosis that lead to pulmonary dysfunction. Anesthesia plan in patient needs to rule out any anomalies. For airway management, Laryngeal mask airway (LMA) should be preferred to avoid the use of muscle relaxants. The use of short-acting anesthetics can accelerate recovery from anesthesia. To reduce postoperative pain, regional techniques are preferred. We report a 6-month- old boy with PBS, and its airway management and anesthesia during surgery.
- Prune belly syndrome
- General anesthesia
- Regional anesthesia
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References
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