Anesthesia management in a pediatric patient with Prune belly syndrome; a case report
Iranian Journal of Pediatric Surgery,
Vol. 8 No. 2 (2022),
Prune belly syndrome (PBS) is a rare congenital disorder, consists of three symptoms: anterior abdominal muscle deficiency, cryptorchidism, and genitourinary malformation. These patients have cardiovascular and musculoskeletal abnormalities, mental retardation, chest deformities, and scoliosis that lead to pulmonary dysfunction. Anesthesia plan in patient needs to rule out any anomalies. For airway management, Laryngeal mask airway (LMA) should be preferred to avoid the use of muscle relaxants. The use of short-acting anesthetics can accelerate recovery from anesthesia. To reduce postoperative pain, regional techniques are preferred. We report a 6-month- old boy with PBS, and its airway management and anesthesia during surgery.
- Prune belly syndrome
- General anesthesia
- Regional anesthesia
How to Cite
Hassett S, Smith GH, Holland AJ: Prune belly syndrome. Pediatric surgery international 2012; 28: 219-228.
Yoon J, Ryu J, Kim J, et al: Anesthetic experience of a patient with Prune-belly syndrome. Korean journal of anesthesiology 2014; 67: 94-96.
Henderson AM, Vallis CJ, Sumner E: Anaesthesia in the prune‐belly syndrome: A review of 36 cases. Anaesthesia 1987; 42: 54-60.
Garg C, Khanna S, Mehta Y: Quadratus lumborum block for postoperative pain relief inpatient with Prune belly syndrome. Indian Journal of Anesthesia 2017; 61:840-843.
Andropoulos DB, Gregory GA: Gregory's Pediatric Anesthesia. John Wiley & Sons, 2020.Strand WR: Initial management of complex pediatric disorders: prune belly syndrome, posterior urethral valves. The Urologic Clinics of North America 2004;31: 399-415.
Bariş S, Karakaya D, Üstün E, et al: Complicated airway management in a child with the prune‐belly syndrome. Pediatric Anesthesia 2001; 11:501-504.
- Abstract Viewed: 58 times
- PDF Downloaded: 44 times