Fibrous Dysplasia of the Orbit in a 5-Year-Old Girl
Journal of Ophthalmic and Optometric Sciences,
Vol. 1 No. 2 (2017),
12 March 2017
,
Page 40-44
https://doi.org/10.22037/joos.v1i2.18489
Abstract
Purpose: The aim of the present study was to describe a case of
orbital fibrous dysplasia in a very young child.
Case report: A 5-year-old girl presented with unilateral, painless,
slowly progressive proptosis of the left eye and inferotemporal
globe displacement from about 1 year ago. The visual acuity in
both eyes was 20/20. The general physical examination was normal.
Computed tomography (CT scan) revealed thickening and deformity
of the orbital walls. Lateral orbitotomy and biopsy were performed
and were compatible with fibrous dysplasia.
Conclusion: Craniofacial fibrous dysplasia usually occurs in the
second decade of life, but it can also rarely present in the early
years of life. Therefore, fibrous dysplasia should be considered as
a differential diagnosis of proptosis or globe displacement in the
early years of life.
Keywords: Fibrous; Dysplasia; Orbit; Child; Iran.
How to Cite
References
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