Delay presentation of congenital diaphragmatic hernia with gastrointestinal manifestations: A case report
Iranian Journal of Pediatric Surgery,
Vol. 5 No. 1 (2019),
15 June 2019
Congenital diaphragmatic hernia (CDH) is usually accompanied by pulmonary hypoplasia, pulmonary hypertension, and other associated anomalies which result in high mortality rates in these cases. This condition occurs when there is a defect in the diaphragm (mostly to the left and posterolateral) from which herniation of the abdominal contents into the thorax can take place. Morgagni hernia is a less common CDH (only 5-10% of CDH cases), in which congenital herniation of the abdominal content through the triangular parasternal gaps of the anterior diaphragm happen. Morgagni hernia usually affects the right side, and the patients are usually asymptomatic. Herein, we present the case of a 15-month-old male infant with large Morgagni hernia resulting in poor weight gain. The presentation was unique due to its huge orifice, its gastrointestinal obstruction presentation and also its unremarkable radiologic findings. The patient was monitored by the follow up team for 12 months. The follow-up revealed no recurrence, and the patient had favorable weight gain without any gastrointestinal symptoms.
- Morgagni hernia
- Diaphragmatic hernia
- Surgical treatment
Mallikarjunappa B, Ashish SR: Congenital Diaphragmatic Hernia: A Case Report. JIMSA
Doyle NM, Lally KP. The CDH Study Group and advances in the clinical care of the patient with congenital diaphragmatic hernia. In Seminars in perinatology 2004;28(3),174-184. WB Saunders.
Rodríguez HJ, Tuca RF, Ruiz FB, et al: Diaphragmatic hernia of Morgagni-Larrey in adults: analysis of 10 cases. Gastroenterología y hepatología 2003;26(9):535-40.
Eren S, Çiriş F: Diaphragmatic hernia: diagnostic approaches with review of the literature. European journal of radiology 2005;54(3):448-59.
Nasr A, Fecteau A: Foramen of Morgagni hernia: presentation and treatment. Thoracic surgery clinics 2009;19(4):463-8.
Elhalaby EA, Sikeena MH: Delayed presentation of congenital diaphragmatic hernia. Pediatric surgery international 2002;18(5-6):480-5.
Loong TP, Kocher HM: Clinical presentation and operative repair of hernia of Morgagni.
Postgraduate medical journal 2005;81(951):41-4.
Nason LK, Walker CM, McNeeley MF, et al: Imaging of the diaphragm: anatomy and function. Radiographics 2012;32(2):E51-70.
Boloker J, Bateman DA, Wung JT, et al: Congenital diaphragmatic hernia in 120 infants treated consecutively with permissive hypercapnea/spontaneous respiration/elective repair. Journal of pediatric surgery 2002;37(3):357-66.
Gander JW, Fisher JC, Gross ER, et al: Early recurrence of congenital diaphragmatic hernia is higher after thoracoscopic than open repair: a single institutional study. Journal of pediatric surgery 2011;46(7):1303-8.
Kesieme EB, Kesieme CN: Congenital Diaphragmatic Hernia: Review of Current Concept in Surgical Management. ISRN Surgery 2011. 2011: p. 8.
Leshen M, Richardson R: Bilateral Morgagni Hernia: A Unique Presentation of a Rare Pathology. Case Reports in Radiology 2016.
McMahon CJ, Taylor MD, Cassady CI, et al: Diagnosis of pentalogy of Cantrell in the fetus using magnetic resonance imaging and ultrasound. Pediatric cardiology 2007;28(3):172-5.
Minneci PC, Deans KJ, Kim P, et al: Foramen of Morgagni hernia: changes in diagnosis and treatment. The Annals of thoracic surgery 2004;77(6):1956-9.
Yap KH, Jones M: Late presentation of congenital diaphragmatic Hernia after a diagnostic laparoscopic surgery (a case report). Journal of cardiothoracic surgery 2013;8(1):8.
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