The role of connective tissue genomics in ascending aortic dissection: A case of Marfan syndrome
Journal of Cellular & Molecular Anesthesia,
Vol. 4 No. 3 (2019),
28 Bahman 2020
,
Page 100-104
https://doi.org/10.22037/jcma.v4i3.28189
Abstract
Background: Aortic dissection is a rare yet life threating condition with some already discovered risk factors namely hypertension, connective tissue disorders such as Marfan syndrome (MFS), cocaine abuse and cigarette smoking.Case report: In this article we would like to present a case of MFS who presented with severe chest pain and undergone Bentall surgery due to aortic dissection and aneurysm.Conclusion: Although many risk factors and preventive measures are already investigated, there is no definite method to avoid its occurrence in genetically predisposed patients such as MFS. Patient-specific models utilizing embryonic stem cells (ESC) and induced pluripotent stem cells (iPSC) may offer some advantages.- Marfan syndrome - Aortic dissection - iPSC - cocaine
How to Cite
References
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