A bizarre presentation of Peutz – jegher’s syndrome in a 2 year old

Amir Molaei--- Assistant professor of general surgery, Semnan university of medical science, resident of plastic surgery, Shahid Beheshti university of medical science, Iran,Tehran.,
Hamidreza Alizadeh Otaghvar--- Associate professor of general surgery , Iran university of medical science , resident of plastic surgery , Shahid Beheshti university of medical science, Iran, Tehran.,
Mohammadreza Tarahomi--- Assistant professor of plastic surgery department, Shahid Beheshti university of medical science, Iran, Tehran.,
Daryanaz Shojaei--- 6th year medical student, Iran university of medical sciences, Iran, Tehran.,
Leili Mohajerzadeh--- Pediatric Surgery Research Center, Shahid Beheshti University of Medical Sciences, Tehran,
Maryam Baghoori--- General practitioner, Shahid Beheshti university of medical science, Iran, Tehran.

Abstract


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Abstract:

Peutz - jegher syndrome  is  pare  autosomal  dominant  disorder  pointed  with  gastro  intestinal and  mucosal  pigmentation.

We present  2 y/o boy with hesion  prolapsed from  rectum  that  non reducted in  study we found  pathology  of PJS and  familial  history  of PJS in  parent.


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References


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DOI: http://dx.doi.org/10.22037/irjps.v3i2.11894

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