A bizarre presentation of Peutz – jegher’s syndrome in a 2 year old

Amir Molaei, Hamidreza Alizadeh Otaghvar, Mohammadreza Tarahomi, Daryanaz Shojaei, Leili Mohajerzadeh, Maryam Baghoori




Peutz - jegher syndrome  is  pare  autosomal  dominant  disorder  pointed  with  gastro  intestinal and  mucosal  pigmentation.

We present  2 y/o boy with hesion  prolapsed from  rectum  that  non reducted in  study we found  pathology  of PJS and  familial  history  of PJS in  parent.

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DOI: https://doi.org/10.22037/irjps.v3i2.11894


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