Rare Phallus Malformations in Children

Javad Ghoroubi, Alireza Mirshemirani, Fatollah Roshanzamir

Abstract


412

Introduction: Penile agenesis (PA) and diphallus (DP) are extremely rare genital anomaly in children. Numerous associated anomalies have been described with these malformations. These patients need several investigations and finally surgical intervention.

Material & Methods: In a retrospective study, 14 patients who were treated for phallus malformation in Mofid Children’s Hospital from January 2004 to December 2013 were studied. Detailed history was taken and para clinical examinations were performed in each patient and diagnosis was confirmed by laboratory tests, abdominal ultrasonography, voiding cystourethrography (VCUG), and karyotype study. Data regarding age, sex, clinical findings, associated anomalies and treatment were collected.

Results: From 14 patients, eight cases had PA (aged 2 to 4320days), and six had DP (aged 2 to 5040 days).Karyotype in all PA’s patients was 46XY. Five of DP cases had completed, and one had bifid phallus type. All patients were treated surgically after complete investigations, and followed within period of study.

Conclusion: All patients with phallus anomalies need extensive evaluations and surgical intervention. No surgical intervention should take place without counseling the parents.


Keywords


penile agenesis; diphallus; treatment; outcome

Full Text:

PDF

416

References


Kessler WO, McLaughlin AP: Agenesis ofpenis. Embryology and management.Urology 1973; 1(3):226-9.

Berry SA, Johnson DE, Thompson TR: Agenesis of penis, scrotal raphe, and anus in one of monoamniotic twins. Teratology. 1984; 29(2):173-6.

Gautier T, Slient J, Pena S, et al. Testicular function in 2 cases of penile agenesis. JUrol. 1981; 126(4):556-7.

Ciftci AO, Senocak ME, Buyuk-pamukcu N: Male gender assignment in penile agenesis: A case report and review of the literature. J Pediatr Surg. 1995; 30(9):1358-60.

Soderdahl DW, Brosman SA, Goodwin WE: Penile agenesis.J Urol. 1972; 108(3):496-9.

Akoz T, Erdogan B, Gorgu M, et al: Penile reconstruction in children using a double vascular pedicle composite groin flap. Scand J UrolNephrol. 1998; 32(3):225-30.

Stolar CJH, Wiener ES, Hersale TW et al: Reconstruction of penile agenesis by a posterior sagittal approach. J Ped Surg.1987; 22(12):1076-80.

Skoog SJ, Belman AB: Aphallia: its classification and management, J Urol.1989; 141(3):589-92.

Gilbert DA, Jordan GH, Devine CJ, et al: Phallic construction in prepubertal and adolescent boys. J Urol. 1993; 149(6):1521-9.

Oesche IL, Pinter A, Ransley PG: Penile agenesis: a report of six cases. JPedSurg.1987;22(2):172-4.

O’Connar TA, LaCour ML, Friendlader ER, et al : Penile agenesis associated with urethral and bilateral renal agenesis.Urology. 1993; 41(6):564-5.

Torres-Medina E, Sanchez-Puente JC, Aragon- Tovar A. Diphallia, report of one case and review of literature. Rev Mex Urol. 2009; 69(1):32-5.

Sharma KK, Jain R, Jain SK, et al: Concealed diphallus: a case report and review of the literature. JIAPS. 2000; 5(1):18-21.

Nesbit RM, Bromme W: Double penis and double bladder with report of a case. Am J Roentgen.1933; 30:497.

Carvalho AP, Ramires R, Soares J, et al: Surgical treatment of complete penile duplication. Actas Urol Esp. 2008; 32(9):941-4.

Tolat SN, Gharpuray MB: Diphallus – a rare congenital anomaly of the penis. Indian J Rare Phallus Malformations in Children Ghoroubi et al. 75 Iranian Journal of Pediatric Surgery Vol. 1 No. 2/2015 DermatolVenereolLeorol. 1991; 57(6):301-2.

Tepeler A, Karadag MA, Sari E, et al : Complete diphallus in a 14 year old boy. Marmara Med J. 2007; 20(3); 190-2.

Priyadarshi S: Diphallus with ectopic bowel segment: a case report. PediatSurg Int. 2005; 21(8):681-3.

Mutlu N, Baykal M, Merder E: Diphallus with urethral duplications. IntUrlNeph. 1999; 31(2):253-5.

Roth JK, Marshall RH, Angel JR, et al: Congenital absence of penis. Urology.1981; 17(6):579-83. 21. Skandalakis JE, Gray SW, Broacher B: The male reproductive tract. In Skandalakis JE, Gray SW (eds): The Embryonic Basis for the Treatment of Congenital anomalies. Baltimore: Williams’s and Wilkins, 1994; Pp: 733-77, 789-91.

Gilbert J, Clark RD, Koyle MA: Penile agenesis: a fatal variation of an uncommon lesion. J Urol. 1990; 143(2):338-9.

Kessler WO, McLaughlin AP. Agenesis of penis embryology and management. Urology 1973;1(3):226-9.

Gluer S, Fuchs J, Mildenberger H: Diagnosis and current management of penile agenesis. J Ped Surg. 1998; 33(4):628-31.

Bruch SW, Meuli M, Harrison MR: Immediate reconstruction for penile agenesis. J Ped Surg. 1996; 31(8):1152-4.

Perovic S: Phalloplasty in children and adolescents using the extended pedicle island groin flap. J Ural. 1995; 154(2 pt 2):848- 53.

Chibber PJ, Shah HN, Jain P, et al: Male gender assignment in aphallia: a case report and review of the literature. IntUrolNephrol. 2005; 37(2):317-9.

Bangroo AK, Khetri R, Tiwari Sh: Penile agenesis. J Indian Asso Pediatr Surg. 2005; 10(4):256-7.

Jeffcoate TNA: A case of diphallus in the female. JObst Gyn. 1952; 7(6):844.

Vilanova X, Raventos A: Pseudodiphallia a rare anomaly. J Urol. 1954; 71(3):338-46.

Bhat H, Sukumar S, Nair T, et al : Successful surgical correction of true diphallia, scrotal duplication and associated hypopadias. J PediatSurg. 2006; 41(10):e13-4.

Djordjevic M, Perovic S: Complete penile joining in a case of wide penile duplication. J Urology.2005; 173(2):587-8.

Gentileschi S, Bracaglia R, Seccia A, et al: Duplication of the glans penis manifested at puberty. J Plastic Recons Surg. 2006; 59(8):882-4.




DOI: https://doi.org/10.22037/irjps.v1i2.11531

Refbacks

  • There are currently no refbacks.


pISSN: 2423-5067

eISSN: 2423-7612

Creative Commons License
This journal and its contents are licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.